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Chronic Pulmonary Hypertension and Congenital Heart Disease

Abstract

Zbigniew Gaciong

A mean pulmonary arterial pressure (MAP) of less than 25 mmHg is regarded as pulmonary hypertension. We examine pathogenesis, diagnosis, and treatment with a focus on their applicability to congenital heart disease. The prevalence of pulmonary hypertension in adults ranges from 5 to 10%, making it a rather common consequence of congenital heart disease. The size and kind of the heart abnormality, as well as hereditary and environmental variables, all play a part in the multifactorial cause that is acknowledged. Instead of the pure Eisenmenger complex, more complex disease is becoming more widely acknowledged. Increased pulmonary vascular resistance, which is brought on by remodelling of the pulmonary vascular bed, can be identified using a range of tests, including echocardiography, exercise testing, cardiac catheterization, MRI, and CT scanning. Medications that treat disease are employed in management, and their effectiveness is rising.