临床和医疗病例报告

Primary Synovial Sarcoma of the Lung: A Very Rare Diagnosis with Poor Prognosis

Abstract

Maria Joao Vieira Silva, Christine Costa and Salvato Feijo

Primary synovial sarcoma of the lung is an extremely rare neoplasm and highly aggressive. The diagnosis is established after extra-thoracic sarcoma and other primary lung malignancies are excluded.

We report the case of a 73-year-old man who presented a well-defined mass. Immunohistochemically was positive for bcl-2, vimentin, S-100 but negative for CD34, cytokeratin, epithelial membrane antigen and calretinin.

Given the rarity of primary synovial sarcoma of the lung, there are no guidelines for its treatment and survival is low although new therapeutic possibilities are upcoming and should be considered in future management.