El?bieta Radzikowska?Katarzyna B?asi?ska-Przerwa?Paulina Skro?ska?El??bieta Wiatr?Tomasz ?witaj?Agnieszka Skoczylas ? Kazimierz Roszkowski-?????li?...?
??????????? (LAM) ???????????????????????????????????? PEComa ?????????????????????????????????????????????????????? LAM?????????????????????????????????????????????????????? LAM ??????????????????????? 14 ???? LAM?13 ?????? LAM?1 ??? TSC/LAM?????????????????????????????????????????19±12.99????????10????13?????????????????1?????????????????????????????1603.85 ± 2437.56 cm3 vs. 198.01 ± 315.43 cm3?p=0.00026?????????FVC?FEV1?TLC?DLCO????6MWT ?????514.46 ± 101.72 m vs. 526.79 ± 139.33 m?p=0.002???????68.93 ± 13.6 mmHg vs. 78.23 ± 11.14 mmHg?p=0.04???? VEGF-D ?????2591 ± 1085 pg/mL vs. 1274 ± 708 pg/mL?p=0.003??????????????????LAM???????????????????????
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???????????????? (BCT) ????????? (RM) ???????????????????? 1986 ? 3 ?? 1989 ????????? 117 ???????? 2 ??????66 ????????????? 51 ???????????????????????????????????????????????????????????????????????????????????????????????????????????????????????????? 240 ??????? (BCT) ??????? (SD±) ? 201.34 ?? (54.12 ± 226.5)???????????????? (SD±) ? 195.84 ?? (35.1 ± 226.5)???????? (p=0.5410)????? (?????p=0.117) ?????? (?????p=0.809) ??????????????????????????????? 211.4 ???95% ????? 197.9*224.9??????????? 204.0 ???95% ????? 188.0*219.9?Log Rank?p=0.342??????????????????? I ???????????????????????????????